Ichthyosis bullosa of Siemens disease as IBS. Ichthyosis bullosa of Siemens Ichthyosis bullosa of Siemens is a type of familial, autosomal dominant ichthyosis, a rare skin disorder. It is also known as bullous congenital ichthyosiform erythroderma of Siemens or ichthyosis exfoliativa. It is a genetic disorder with no known cure which is estimated to affect about 1 in 500,000 people. IBS has symptoms very similar to epidermolytic hyperkeratosis (EHK) but is generally milder than EHK. IBS affects only the upper layers of the epidermis whilst EHK affects the suprabasal layer which is deeper in the skin. At birth the baby's skin has a red
The Bringers of Wonder, Part One Koenig, Helena gives as good as she gets. Across the room, Vincent is showing Louisa one of the remote medical relays which allow them to monitor patients from anywhere on the base. He observes Koenig's obvious distress, but Louisa stares into his eyes and he, in a trance-like state, switches off the monitor. When the girl is swept away by Carter, Vincent's head clears. Reactivating the screen, he observes Koenig's condition and dashes from the room. Koenig is convulsing by the time Vincent reaches Medical. He throws the orderly away from the brain complex, but the man attacks him with