Ichthyosis bullosa of Siemens present. A distinctive characteristic of IBS which is not present in other forms of ichthyosis is called the "Mauserung phenomenon" (Mauserung is German for "moulting" and was first described by H.W.Siemens). These are small patches of bare, apparently normal skin in the middle of areas of hyperkeratosis. As the sufferer ages the flaking and blistering should improve. The hyperkeratosis may grow more severe but more localized and is generally only present on flexural folds of the major joints. IBS is an autosomal dominant genetic condition caused by a mutation in the gene for keratin 2e on chromosome 12. This means
Sound Affects Sound Affects Sound Affects is the fifth studio album by British rock band the Jam. The cover art is a pastiche of the artwork used on various "Sound Effects" records produced by the BBC during the 1970s. It is their only album co-produced by the band, and contains the only album track co-written by the entire band, "Music for the Last Couple". The album was released on 28 November 1980. Paul Weller is known to have opined "Sound Affects" as the best album The Jam released throughout their career; freely admitting the Beatles' "Revolver" had been a major influence upon