Ichthyosis bullosa of Siemens Ichthyosis bullosa of Siemens Ichthyosis bullosa of Siemens is a type of familial, autosomal dominant ichthyosis, a rare skin disorder. It is also known as bullous congenital ichthyosiform erythroderma of Siemens or ichthyosis exfoliativa. It is a genetic disorder with no known cure which is estimated to affect about 1 in 500,000 people. IBS has symptoms very similar to epidermolytic hyperkeratosis (EHK) but is generally milder than EHK. IBS affects only the upper layers of the epidermis whilst EHK affects the suprabasal layer which is deeper in the skin. At birth the baby's skin has a red appearance like a
Supernumerary body part sometimes represented as having numerous breasts. This was particularly notable in the cult of Artemis (Diana) celebrated in the ancient city of Ephesus, in modern Turkey. In Japanese mythology, the god of the sea and storms, Susanoo, is sometimes depicted as having a third arm. In Hungarian mythology, having six fingers on a hand (polydactyly) is held to be the sign of innate supernatural power (see táltos). In the Bible, Goliath has brothers who have six fingers and six toes. Supernumerary body part Supernumerary body parts are most commonly a congenital disorder involving the growth of an additional part of